(1) succinyl-CoA@mitochondrial intermembrane space+glycine@mitochondrial intermembrane space - ALAS*:pyridoxal 5'-phosphate@mitochondrial intermembrane space -> 5 aminolevulinic acid@mitochondrial intermembrane space+CO_sub_2_endsub_@mitochondrial intermembrane space+coenzyme A@mitochondrial intermembrane space
(2) ALAS*@mitochondrial intermembrane space -> ALAS*:pyridoxal 5'-phosphate@mitochondrial intermembrane space