(1) 5 aminolevulinic acid - ALAD:Zn2+:succinylacetone - ALAD:Zn2+:succinylacetone -> porphobilinogen (2) porphobilinogen - HMBS -> hydroxymethylbilane+NH3
ChEBI 8335 KEGGCOMPOUND C00931 CAS 487-90-1